EVALUATION OF COCHLEAR IMPLANT SURGERY RESULTS IN PATIENTS WITH COCHLEAR MALFORMATIONS AT CHIDREN HOSPITAL 1

Tuan Nhu Nguyen1, , Huu Dang Luong2, Nguyen Thai Pham1, Tuong Vinh Tran2, Doan Tan Tai Pham1
1 Bệnh viện Nhi Đồng 1
2 Đại học Y Dược TP. Hồ Chí Minh

Main Article Content

Abstract

Objective: We describe one case of bilateral cochlear implantation in a child with cochlear malformation at Nhi Dong 1 Hospital and provide an initial assessment of the treatment outcomes post-surgery.

Subjects and Methods: A case report.

Results: A 2-year-old female patient has been diagnosed with bilateral Mondini type I cochlear malformation. Before the surgery, her condition was very serious, with an average hearing threshold reaching 95 dB, resulting in a loss of hearing and significantly affecting her language development. After a comprehensive evaluation, she was indicated for cochlear implant surgery. The electrodes were designed to be shorter, with an active stimulation range of 14.3 mm, a base diameter of 0.8 mm, and an apex diameter of 0.5 mm, to fit and optimize for the child's cochlear structure. Post-surgery, the wound healed well, and no complications were recorded. Notably, after 7 months of right ear tuning, her PTA (pure tone audiometry) threshold improved to 46.3 dB, and after 5 months of left ear tuning, the PTA threshold was 56.3 dB, showing significant improvement. The results of language development after surgery are also very positive, she can hear basic sounds clearly and recognize objects, demonstrating significant progress in her ability to understand and use language, similar to other children who have received cochlear implants.

Conclusion: The case of cochlear implantation in the 2-year-old patient with bilateral cochlear deformity demonstrates a positive impact on improving hearing and language development. Early intervention has enabled the child to recover well after surgery and achieve significant advancements in communication. This underscores the importance of timely diagnosis and treatment for children with congenital hearing loss, thereby opening up opportunities for their comprehensive development in the future.

 

Article Details

References

1.           Balkany TJ, Hodges AV, Eshraghi AA, Butts S, Bricker K, Lingvai J, et al. Cochlear Implants in Children- A Review. Acta Otolaryngol. 2002;122:356-362. Doi: 10.1080/00016480260000012.

2.         Sainz M, Skarzynski H, Allum JHJ, et al. Assessment of Auditory Skills in 140 Cochlear Implant Children Using the EARS Protocol. ORL. 2003;65(2):91-96. doi:10.1159/000070772

3.         Deep, N.L, Dowling E.M, Jethanamest D, Carlson ML. Cochlear Implantation: An Overview. Journal of Neurological Surgery Part B; Skull Base. Apr 2019; 80(2):169-177. doi:10.1055/s-0038-1669411.

4.         Gifford   RHJTHJ.   Two-eared   Hearing No  Longer  Experimental.  LWW;  2019. p. 6-7.

5.         Sennaroglu L, Saatci I. A New Classification for Cochleovestibular Malformations. Laryngoscope. 2002;112:2230-2241. Doi: 10.1097/00005537-200212000-00019.

6.         Kröger S, Glaubitz C, Kronesser D, et al. Auditory and language development in children with bilateral cochlear implants (CI) – a multicentric, retrospective longitudinal analysis. In: Laryngo-Rhino-Otologie. Vol 102. Georg Thieme Verlag; 2023. doi:10.1055/s-0043-1767524

7.         Suri NM, Prasad AR, Sayani RK, Anand A, Jaychandran G. Cochlear implantation in children with Mondini dysplasia: our experience. J Laryngol Otol. 2021;135(2):125-129. doi:10.1017/S0022215121000372

8.         Teplitzky T, Lee K. Cochlear Implants in Children with Inner Ear Malformations, A Review of Current Literature. Med Res Arch. 2022;10. doi:10.18103/mra.v10i5.2845