UPDATE ON CONGENITAL CHOLESTEATOMA DIAGNOSIS AND TREATMENT

Thi Hong Ninh Chu1, , Tien Truong Dang, Duc Thuan Nghiem, Thi Hong Hoa Doan
1 Bệnh viện Quân y 103, Học viện Quân y

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Abstract

Background: Congenital cholesteatoma was a rare disorder. Diagnosis and treatment of congenital cholesteatoma still was difficult. Objective: This article updated the information and knowledge on diagnosis and treatment of cholesteatoma. Method: The literature search was undertaken with PubMed as well as published studies on ranked publications. The search terms "congenital cholesteatoma", "update", "diagnosis and treatment" were used to acquire the information. Results: Congenital cholesteatomas have been defined as pearl white cholesteatoma mass in intact tympanic membrane with evidencing no prior history of otorrhea, tympanic perforation, or previous otologic procedures. The pathogenesis of congenital cholesteatoma remains controversial; however, the most commonly accepted theory was a epithelial rest theory. The incidence of this disorder likely is increasing. The most common locations of cholesteatoma were the anterior-superior and posterior-superior quadrants of the eardrum. Conductive hearing loss was the most common symptom. Classification systems based on disease staging have recently been improved in order to unify and identify the disease status. The congenital cholesteatoma treatment was still surgical approach. A second-look approach for treating congenital cholesteatoma was considered for individual case. Conclusion: Congenital cholesteatoma is a pearly white mass of cholesteatoma. Diagnosis was often delayed, complications were often dangerous and treatment was difficult. Updated information on the diagnosis and treatment of congenital cholesteatoma contributes to helping otolaryngologists improve their vigilance in diagnosing and treating the disease more effectively.

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References

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